1985 [10] | F/24 | Abdominal pain and distension, fever, arthralgia, skin ulceration | Hb 9 g/dL, ESR 110 mm/hr | Pericardial effusion |
Anti-nuclear factor(+) 1:540 |
1995 [7] | F/42 | Abdominal distension | Hb 10.0 g/dL, ESR 130 mm/hr, CRP 1.71 mg/dL | Ascites |
ANA(+) 1:640, anti-RNP(+), anti-sm Ab(+), anti-Ro/La(+/+) |
1999 [11] | F/18 | Abdominal pain and distension | Hb 16.4 g/dL | Ascites |
ANA(+) 1:40, anti-DNA Ab(+) 11.6 IU/m L |
2000 [8] | F/33 | Abdominal pain and distension, diarrhea, nausea, anorexia, fever, weight loss | Hb 9.3 g/dL, ESR 20 mm/hr | Ascites, bowel wall thickening (small) |
ANA(+), anti-dsDNA Ab(+) |
2006 [12] | F/21 | Generalized swelling, | Hb 10.1 g/dL, ESR 40 mm/hr | Ascites, pleural effusion, edematous pancreas |
Abdominal pain and distension | ANA(+)1:80, anti-dsDNA Ab(+) 95 IU/ml |
2011 [13] | F/49 | Nausea/vomiting, abdominal pain and distension | Hb 11.4 g/dL, ESR 47 mm/hr, CRP 0.2 mg/dL | Ascites, bowel wall swelling (small/large/rectum) |
ANA(+) 1:80, anti-dsDNA Ab(+) 1:10 |
2011 [4] | F/18 | Anorexia, vomiting, diarrhea, abdominal distension | CRP 24.4 mg/L, amylase/lipase elevation | Ascites, bowel wall thickening and edema (small/large) |
ANA(+) 1:5120, anti-Ro(+), anti-dsDNA Ab(+) 1:80 |
2012 [14] | F/45 | Abdominal pain and distension, pretibial pitting edema | Hb 10.5 g/dL, ESR 40 mm/hr, CRP 0.47 mg/dL | Ascites, bowel wall swelling and distension (small/large) |
ANA(+) 1:1280, anti-Ro/La(+/+), anti-dsDNA Ab(+) 20 IU/ml |
2012 [15] | F/22 | Fever, diarrhea, vomiting, abdominal pain and distension | Hb 13.3 g/dL, ESR 9 mm/hr, CRP 11.1 mg/L | Thickened bowel loops, dilated renal pelvis |
ANA(+) 1:320, anti-dsDNA Ab(+) 28 IU/ml |