Table 3. Differential diagnosis of pediatric dyslipidemia

Primary disorders Secondary disorders
Familial hypercholesterolemia Hypothyroidism
Autosomal recessive Diabetes
Hypercholesterolemia Pregnancy
Autosomal dominant Drugs
Hypercholesterolemia Obesity
Familial ligand-defective apoB-100 Alcohol
Sitosterolemia Nephrotic syndrome
Familial combined hyperlipidemia Chronic renal failure
Familial hypertriglyceridemia Cholestasis
Familial chylomicronemia syndrome Biliary atresia
Hypoalphalipoproteinemia Hepatitis
Dysbetalipoproteinemia Biliary cirrhosis
Human immunodeficiency virus infection/acquired immunodeficiency syndrome