We presented here a patient of autoimmune hemolytic anemia associated with systemic lupus erythematosus. This 38 year old female was admitted because of dizziness and dyspnea. In peripheral blood and bone marrow study, characteristics of autoimmune hemolytic anemia were seen. And she was well treated with prednisolone only. The general concept of autoimmune hemolytic anemia with the brief review of literature is discussed.

Primary ciliary dyskinesia is a genetic disorder of abnormal ciliary structure and function that leads to defective mucociliary clearance, resulting in sinopulmonary infection and infertility. Kartagener's syndrome is a subclass of primary ciliary dyskinesia and which is clinically distinguishable by the presence of situs inversus. Electron microscopy of cilia reveals ultrastructural defects in the ciliary axoneme. In the respiratory tract, this inability presumably causes impaired clearance of mucus and inhaled particles and results in the chronic infections of sinuses and bronchial trees that are characterized of the disease. Early diagnosis of the disease may be important for prevention of bronchiectasis and pulmonary insufficiency.

We report one case of primary ciliary dyskinesia associated with Kartagener's syndrome in a 14 year-old young man who was presented as bronchiectasis, chronic and situs inversus, with review of literature.